The urea cycle

The urea cycle. The urea cycle is a pathway of cytosolic and mitochondrial proteins involved in the conversion of ammonia (NH4) to urea for excretion via the kidneys. The enzymes in the pathway are as follows: carbamoylphosphate synthetase (CPS1), ornithine transcarbamylase (OTC); argininosuccinic acid synthase (ASS); argininosuccinic acid lyase (ASL); arginase I (ARG); nitric oxide synthase (NOS). Pearl [].
The urea cycle

Publication

Metabolic Causes of Epileptic Encephalopathy. (2013) Joe Yuezhou Yu, et al. Epilepsy Res Treat. 2013;2013:124934. Figure: F6.

Gene mentions


Organism Group Word Match Source NCBI Symbol NCBI ID
Homo sapiens Primates ATP ATP ncbigene_synonym ATP8A2 51761
Homo sapiens Primates OTC. OTC ncbigene_symbol OTC 5009
Homo sapiens Primates ASS ASS ncbigene_synonym ASS1 445
Homo sapiens Primates NOS NOS ncbigene_synonym NOS1 4842
Homo sapiens Primates NOS NOS ncbigene_synonym NOS2 4843
Homo sapiens Primates NOS NOS famplex_relations NOS3 4846
Homo sapiens Primates ASL ASL ncbigene_symbol ASL 435
Homo sapiens Primates ASL ASL ncbigene_synonym ADSL 158
Homo sapiens Primates ARG ARG ncbigene_synonym ABL2 27
Homo sapiens Primates ARG ARG ncbigene_synonym RERE 473
Mus musculus Rodents OTC. OTC ncbigene_symbol Otc 18416
Mus musculus Rodents ASS ASS ncbigene_synonym Ass1 11898
Mus musculus Rodents NOS NOS ncbigene_synonym Nos1 18125
Mus musculus Rodents ASL ASL ncbigene_symbol Asl 109900
Mus musculus Rodents ASL ASL ncbigene_synonym Adsl 11564
Mus musculus Rodents ARG ARG ncbigene_synonym Abl2 11352
Mus musculus Rodents ARG ARG ncbigene_synonym Rere 68703
Mus musculus Rodents ARG ARG ncbigene_synonym Albfm1 622307
Drosophila melanogaster Invertebrates ATP ATP ncbigene_synonym ATPsynbeta 43829
Drosophila melanogaster Invertebrates ATP ATP ncbigene_synonym Atpalpha 48971
Drosophila melanogaster Invertebrates ASS ASS ncbigene_symbol Ass 40812
Drosophila melanogaster Invertebrates NOS NOS ncbigene_symbol Nos 34495
Drosophila melanogaster Invertebrates NOS NOS ncbigene_symbol nos 42297
Drosophila melanogaster Invertebrates ASL ASL ncbigene_symbol asl 40682
Drosophila melanogaster Invertebrates ARG ARG ncbigene_symbol arg 46717
Drosophila melanogaster Invertebrates ARG ARG ncbigene_synonym aos 39833

Chemical mentions

Word Match MeSH Name ChEBI
Arginine Arginine mesh:D001120 arginine chebi:29016
ARG Arginine mesh:D001120 arginine chebi:29016
Aspartate NA mesh:D001224
Fumarate NA mesh:D005650
phosphate NA mesh:D010710

Disease mentions

Word Match MeSH Name DOID