CoQ10biosynthetic pathway with eight known biosynthetic enzymes denoted as COQ1–COQ8

CoQ10biosynthetic pathway with eight known biosynthetic enzymes denoted as COQ1–COQ8. COQ2, decaprenyl-4-hydroxybenzoate transferase, mediates the conjugation of the benzoquinone ring with the decaprenyl side chain.
CoQ10biosynthetic pathway with eight known biosynthetic enzymes denoted as COQ1–COQ8
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Publication

A Mutation in Para-Hydroxybenzoate-Polyprenyl Transferase (COQ2) Causes Primary Coenzyme Q10 Deficiency. (2006) Catarina Quinzii, et al. Am J Hum Genet. 2006 Feb;78(2):345-349. Figure: F1.

Gene mentions


Organism Group Word Match Source NCBI Symbol NCBI ID
Homo sapiens Primates COQ1 COQ1 ncbigene_synonym PDSS1 23590
Homo sapiens Primates COQ2 COQ2 ncbigene_symbol COQ2 27235
Homo sapiens Primates COQ3 COQ3 ncbigene_symbol COQ3 51805
Homo sapiens Primates SAH SAH ncbigene_synonym ACSM3 6296
Homo sapiens Primates COQ6 COQ6 ncbigene_symbol COQ6 51004
Homo sapiens Primates COQ5 COQ5 ncbigene_symbol COQ5 84274
Homo sapiens Primates COQ7 COQ7 ncbigene_symbol COQ7 10229
Drosophila melanogaster Invertebrates COQ2 COQ2 ncbigene_symbol Coq2 40988
Drosophila melanogaster Invertebrates COQ? COQ ncbigene_symbol coq 45984
Drosophila melanogaster Invertebrates COQ3 COQ3 ncbigene_symbol Coq3 35383
Drosophila melanogaster Invertebrates SAM SAM ncbigene_symbol sam 44534
Drosophila melanogaster Invertebrates SAM SAM ncbigene_synonym qkr54B 36966
Drosophila melanogaster Invertebrates SAM SAM ncbigene_synonym sls 44013
Drosophila melanogaster Invertebrates SAM SAM ncbigene_synonym Sam-S 48552
Drosophila melanogaster Invertebrates SAH SAH ncbigene_symbol sah 5658327
Drosophila melanogaster Invertebrates COQ6 COQ6 ncbigene_symbol Coq6 33777
Drosophila melanogaster Invertebrates COQ5 COQ5 ncbigene_symbol Coq5 32272
Drosophila melanogaster Invertebrates COQ7 COQ7 ncbigene_symbol Coq7 44007

Chemical mentions

Word Match MeSH Name ChEBI

Disease mentions

Word Match MeSH Name DOID